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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2020; 30(03): 395-399
DOI: 10.4103/ijri.IJRI_165_19
Case Report

A case of dorsal agenesis of pancreas associated with unilateral renal agenesis, unicornuate uterus, and ovarian ectopia: A brief review and learning points

Arindam Bhandari
Department of Radiology, Kothari Medical Centre, Kolkata, West Bengal, India
,
Samrat Mandal
Department of Radiology, Kothari Medical Centre, Kolkata, West Bengal, India
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Abstract

Dorsal agenesis of the pancreas is a rare entity, with about 100 cases reported. It can be overlooked on ultrasound due to the non visualization of the body and tail of the pancreas.This is due to overlying gas in the stomach, which offers a poor acoustic window and obscures visualization. Renal agenesis and Mullerian duct anomalies are uncommon associations of dorsal agenesis of the pancreas because of the separate embryological origin of the pancreas and genitourinary organs. Here, we present a case of a 17-year-old patient who had dorsal agenesis of the pancreas, associated with unilateral renal agenesis, unicornuate uterus, and ectopic ovary. We describe the anomalies and discuss the radiological differential diagnosis and potential pitfalls. We provide a brief review of the literature with few radiological teaching points and possible genetic implications of the case.

Keywords

Dorsal agenesis of pancreas - ectopic ovary - unicornuate uterus - unilateral renal agenesis


Publication History

Received: 05 April 2019

Accepted: 04 June 2020

Article published online:
19 July 2021

© 2020. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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