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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2020; 41(02): 254-256
DOI: 10.4103/ijmpo.ijmpo_93_18
Case Report

Paroxysmal Sympathetic Hyperactivity – An Under-Recognized Entity in Pediatric Brain Tumors: Case Report and Review of Literature

Yamini Krishnan
Department of Paediatric Oncology, MVR Cancer Centre and Research Institute, Kozhikode (Calicut), Kerala, India
,
B Smitha
Department of Paediatric Oncology, MVR Cancer Centre and Research Institute, Kozhikode (Calicut), Kerala, India
,
Shamsudheen Cholayil
Department of Radiation Oncology, MVR Cancer Centre and Research Institute, Kozhikode (Calicut), Kerala, India
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Abstract

Paroxysmal sympathetic hyperactivity (PSH) is not a well-recognized syndrome in pediatric brain tumors, but has been described in adults with traumatic brain injury. We describe the case of a child with medulloblastoma presenting with PSH. An index of suspicion is important in early diagnosis of PSH and this ultimately has an impact on the long-term outcome of patients with the syndrome.

Keywords

Dysautonomia - Medulloblastoma - paroxysmal sympathetic hyperactivity - Pediatric brain tumors


Publication History

Received: 26 April 2018

Accepted: 21 June 2018

Article published online:
23 May 2021

© 2020. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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