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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2019; 40(04): 588-590
DOI: 10.4103/ijmpo.ijmpo_85_18
Practitioner Section

Mucoepidermoid Carcinoma of the Vulva: A Distinct Pathological and Clinical Entity

Satyendra Narayan Sinha
Departments of Medical Oncology, Mahavir Cancer Sansthan, Patna, Bihar, India
,
Brajesh Kumar Choudhary
Departments of Medical Oncology, Mahavir Cancer Sansthan, Patna, Bihar, India
,
Sanjay Kumar
Departments of Pathology, Mahavir Cancer Sansthan, Patna, Bihar, India
,
Manisha Singh
Departments of Medical Oncology, Mahavir Cancer Sansthan, Patna, Bihar, India
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Abstract

Unlike their major salivary gland counterparts, primary mucoepidermoid carcinoma of the vulva is extremely rare tumor. Here, we describe an unusual case of MEC arising from vulva and a short review of literature. This report describes an interesting and unusual case of mucoepidermoid carcinoma of vulva. A 42-year female presented with approx. 3.5 x 3.0 cm size painless polypoidal growth on right labia majora. CT scan abdomen & pelvis showed 30 x 27 cm size well defined lobulated polypoidal lesion is noted in right side of labia majora. Wide local excision had done with margin. Histological evaluation revealed a typical MEC with negative margin. Our tumor board has decided to keep on close follow-up because of the aggressive behaviour of such type of tumour. Follow-up at 6 months has revealed no evidence of recurrence. This is, to our knowledge, the first report of MEC arising from vulva in India. We report a very rare case of primary mucoepidermoid carcinoma of the vulva and this is the first case reported in India. Treatment strategy for MEC vulva yet to decide and patients should be closely followed-up for life to rule out late recurrence.

Keywords

Carcinoma vulva - mucoepidermoid carcinoma - Mucoepidermoid Carcinoma of the Vulva


Publication History

Received: 13 April 2018

Accepted: 21 June 2018

Article published online:
03 June 2021

© 2020. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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