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DOI: 10.4103/ijmpo.ijmpo_74_17
Xeroderma Pigmentosum and Bone Marrow Aplasia: A Rare Association
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Abstract
Xeroderma pigmentosum (XP) is a rare autosomal recessive disorder characterized by hypersensitivity to ultraviolet rays and predisposition to cutaneous malignancies. Hematological disorders associated with XP include myelodysplastic syndrome and acute leukemia. We report a 7-year-old child with XP along with squamous cell carcinoma and bone marrow aplasia.
Publikationsverlauf
Artikel online veröffentlicht:
23. Juni 2021
© 2018. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)
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