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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2017; 38(02): 207-209
DOI: 10.4103/ijmpo.ijmpo_59_16
Case Report

Solid Pseudopapillary Tumor of Pancreas: A Case Report and Review of Literature

Gursev Sandlas
Department of Paediatric Surgery, Kokilaben Dhirubhai Ambani Hospital, Mumbai, Maharashtra, India
,
Charu Tiwari
Department of Paediatric Surgery, TNMC and BYL Nair Hospital, Mumbai, Maharashtra, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Solid pseudopapillary neoplasm of the pancreas is one of the rarest forms of pancreatic neoplasm. It was also known as Franz's tumor or Hamoudi tumor until WHO labeled it as solid pseudopapillary tumor (SPT) in 1996. It typically affects young non-Caucasian females in their second or third decade of life. Treatment involves complete excision of the tumor which results in complete cure in majority of the cases. We present here a report of 11-year-old girl with SPT and also do a review of literature for this rare tumor.

Keywords

Children - Franz's tumour - solid pseudopapillary tumor


Publication History

Article published online:
06 July 2021

© 2017. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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