CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2018; 39(02): 260-262
DOI: 10.4103/ijmpo.ijmpo_135_17
Case Report

Peculiarities of Yolk Sac Tumor in Head and Neck: A Case Report and Literature Review

K Devaraja
Department of Otorhinolaryngology, Kasturba Medical College, Manipal, Karnataka, India
,
Kapil Sikka
Department of Otorhinolaryngology, All India Institute of Medical Sciences, New Delhi, India
,
Pankaj Kumar Singh
Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi, India
› Author Affiliations
Financial support and sponsorship Nil.

Abstract

Yolk sac tumor (YST) is the most common malignant germ cell tumor of head and neck region, constituting around 1% of all malignant germ cells. The rarity of the tumor has led to a relatively sparse collective description of clinical and prognostic factors of such a tumor affecting head and neck region. In this case report with review of the literature, we have highlighted certain peculiar features of YSTs affecting the head and neck region. They seem to commonly affect female children. These tumors seem to fare poorly in children of <1 year of age. Multimodality of treatment consisting of combination chemotherapy with the cisplatin-based regimen and surgery and/or radiotherapy helps in achieving long-term disease-free survival in those affected.



Publication History

Article published online:
23 June 2021

© 2018. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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