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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2018; 39(03): 380-384
DOI: 10.4103/ijmpo.ijmpo_11_16
Practitioner Section

Extraosseous Ewing's Sarcoma of the Maxillary Sinus: A Very Rare Entity

A Ravi Prakash
Department of Oral Pathology and Microbiology, G. Pulla Reddy Dental College and Hospital, Kurnool, Andhra Pradesh, India
,
A Vikram Simha Simha Reddy
Department of Oral Pathology and Microbiology, G. Pulla Reddy Dental College and Hospital, Kurnool, Andhra Pradesh, India
,
Lakshmi Keerthana Killampalli
Department of Oral Pathology and Microbiology, G. Pulla Reddy Dental College and Hospital, Kurnool, Andhra Pradesh, India
,
M Rajinikanth
Department of Oral Pathology and Microbiology, G. Pulla Reddy Dental College and Hospital, Kurnool, Andhra Pradesh, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Ewing's sarcoma is rare sarcoma of bone and soft tissue that uncommonly involve the head and neck in both bone and soft tissue locations. The term Ewing's sarcoma family of tumors comprises both Ewing's sarcoma and peripheral neuroectodermal tumor. It was in 1975, Angervall and Enzinger described the Ewing's sarcoma arising in soft tissues (extraskeletal). The principal sites of extraskeletal Ewing's sarcoma are the paravertebral region and chest wall, generally in close association with vertebrae or the ribs. These tumors may also arise in the soft tissues of the lower extremities and rarely in the pelvic region and hip regions. Superficially located cases do occur but are rare. Here, we present a case of Ewing's sarcoma involving the maxillary sinus region. A 12-year-old boy reported to our department with a swelling on the right side of middle third of the face for 15 days. Intraorally, there was only obliteration of the labial vestibule. On histopathological examination, a provisional diagnosis of malignant round cell tumor was given. Immunohistochemistry with a panel of markers was done to come to a definitive diagnosis. CD99 positivity confirmed the diagnosis of Ewing's sarcoma.

Keywords

Ewing's sarcoma - extraskeletal - maxillary region


Publication History

Article published online:
17 June 2021

© 2018. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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