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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2017; 38(03): 383-386
DOI: 10.4103/ijmpo.ijmpo_108_17
Case Report

Extrarenal Extracranial Rhabdoid Tumor of the Pelvis in a Young Adult‑management of a Challenging Case

Bharti Devnani
Department of Radiotherapy and Oncology, All India Institute of Medical Sciences, New Delhi, India
,
Ahitagni Biswas
Department of Radiotherapy and Oncology, All India Institute of Medical Sciences, New Delhi, India
,
Sameer Bakhshi
Department of Medical Oncology, All India Institute of Medical Sciences, New Delhi, India
,
Seema Kaushal
Department of Pathology, All India Institute of Medical Sciences, New Delhi, India
,
Tripti Nakra
Department of Pathology, All India Institute of Medical Sciences, New Delhi, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Rhabdoid tumor commonly occurs in the kidney and has an aggressive clinical course with high mortality. Central nervous system is the most common extrarenal site. Extrarenal extracranial rhabdoid tumor (EERT) is rare. EERT usually presents in childhood, and presentation in adulthood is extremely rare. This tumor is often difficult to diagnose, and there is no established standard of care due to the paucity of cases. We herein report a case of extrarenal rhabdoid tumor of the pelvis in a young adult and discuss the presentation and possible treatment options of this rare tumor.

Keywords

Extracranial - extrarenal - INI-1 - pelvis - rhabdoid tumor


Publication History

Article published online:
04 July 2021

© 2017. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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