Primary central nervous system lymphoma (PCNSL) is a rare tumor that accounts for
<1%–4% of primary CNS tumor.[[1]] PCNSLs are class of non-Hodgkin's lymphomas which are primarily of diffuse large
B-cell origin (90%), with remaining being T-cell lymphoma (10%). Author report a rare
case of PCNSL presenting as an intracranial mass involving the entire ventricular
system, in an immunocompetent 36-year-old male with severe headache, decreased vision,
and unsteady gait. The diagnosis was obtained by histopathological and subsequent
immunohistochemistry.
Key-words:
Intraventricular lymphoma - primary central nervous system lymphoma