A cavernous venous malformation of the orbit mimicking an idiopathic orbital inflammation

Niphon Chirapapaisan; Chanon Ngamsombat; Jantima Tanboon; Pornsuk Cheunsuchon; Sugamon Koohasawad

doi:10.4103/ajns.AJNS_236_20

Asian Journal of Neurosurgery, Table of Contents

CC BY-NC-ND 4.0 · Asian J Neurosurg 2020; 15(03): 750-752
DOI: 10.4103/ajns.AJNS_236_20

Case Report

A cavernous venous malformation of the orbit mimicking an idiopathic orbital inflammation

Niphon Chirapapaisan

Department of Ophthalmology, Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok

,

Chanon Ngamsombat

¹Department of Radiology, Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok

,

Jantima Tanboon

²Department of Pathology, Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok

,

Pornsuk Cheunsuchon

²Department of Pathology, Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok

,

Sugamon Koohasawad

³Department of Ophthalmology, Prasat Neurological Institute, Bangkok

› Author Affiliations

Abstract

Orbital cavernous venous malformations (CVMs) are usually slow progressing. Multiple CVMs, bilateral orbital CVMs, and acute presentations are rare. We present a rare, bilateral, orbital CVM with acute painful visual loss in the left eye. The initial clinical presentation mimicked an idiopathic orbital inflammation. Orbital magnetic resonance imaging revealed its rare location at the left orbital apex. Finally, pathology confirmed the presence of an intralesional hemorrhage of a CVM.

Key-words:

Cavernous venous malformations - idiopathic orbital inflammation - orbital

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References

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