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CC BY-NC-ND 4.0 · Asian J Neurosurg 2020; 15(01): 190-193
DOI: 10.4103/ajns.AJNS_233_19
Case Report

Cervicomedullary ependymoma with hemorrhage: A case report and review of literature

Raja Kutty
Department of Neurosurgery, Government Medical College, Trivandrum, Kerala
,
Kazumi Ohmori
1   Department of Neurosurgery, Nishinomiya Watanabe Cardiovascular Center, Nishinomiya City, Hyuogo
,
Yasuhiro Yamada
2   Department of Neurosurgery, Bantane Hospital, Fujita Health University, Nagoya, Aichi
,
Yoko Kato
2   Department of Neurosurgery, Bantane Hospital, Fujita Health University, Nagoya, Aichi
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Ependymoma is a rare tumor central nervous system that arises from the ependymal lining of the ventricles or the central canal of the spinal cord. They are of neuroectodermal in origin and constitute about 30%–86% of tumors arising in the spinal cord. The occurrence of these tumors in the cervicomedullary region is very rare. Sudden symptomatic neurologic presentations due to hemorrhage in cervicomedullary ependymoma is very rare and so far have never been reported. Mostly presenting as neurologic deficits involving limbs, these tumors pose a technical challenge in their removal. We present a patient who presented with sudden-onset dysesthesia of the upper and lower limbs. On imaging, he was found to have a cystic medullary tumor extending to the cervical region with hemorrhage. We discuss the epidemiology, surgical challenges, and outcome along with review of literature of these rare tumors located in this precarious location.

Key-words:

Cervicomedullary - ependymoma - hemorrhage

Financial support and sponsorship

Nil.




Publication History

Received: 21 July 2019

Accepted: 21 November 2019

Article published online:
16 August 2022

© 2020. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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