IJNS 2014; 03(02): 125-127
DOI: 10.4103/2277-9167.138924
Case Report
Thieme Medical and Scientific Publishers Private Ltd.

Hirayama disease

Chanabasappa V. Chavadi
Gowtham Jasti
Madhav Hegde
1  Ambedkar Medical College, Bengaluru, Karnataka, India
Anand Venugopal
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18. Januar 2017 (online)


Hirayama disease (HD) is a rare cause of cervical myelopathy often misdiagnosed as motor neuron disease and easily missed on routine magnetic resonance imaging (MRI), at time where detection is crucial to prevent irreversible cord injury. Believed to be a cervical flexion myelopathy, HD differs from motor neuron diseases because of its nonprogressive course and pathologic findings of chronic microcirculatory changes in the lower cervical cord. Dynamic forward displacement of dura in flexion causes asymmetric flattening of lower cervical cord. While dynamic contrast MRI is diagnostic, routine study has high predictive value. A case of HD, etiopathogenesis, imaging and treatment is summarized.