ABSTRACT
Epignathus is an extremely rare oropharyngeal teratoma that commonly arises from the
palate, leading to a high mortality (80-100%) due to airway obstruction in the neonatal
period. We present a case of epignathus immature teratoma with fetiform features,
originating from basisphenoid in a 28-week preterm male baby, who succumbed to death
immediately after birth. Since epignathus is a life-threatening condition at the time
of delivery, a prenatal diagnosis is essential to coordinate the treatment and appropriate
management by securing the airway, either by endotracheal intubation or tracheostomy
followed by complete resection of the tumor.
Keywords
Epignathus - fetiform - immature teratoma - resection
