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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2009; 30(04): 141-143
DOI: 10.4103/0971-5851.65338
CASE REPORT

Mesenchymal hamartoma of the liver

Rahul Gupta
Department of Pediatric Surgery, King Edward Memorial Hospital, Parel, Mumbai, India
,
Sandesh V Parelkar
Department of Pediatric Surgery, King Edward Memorial Hospital, Parel, Mumbai, India
,
Beejal Sanghvi
Department of Pediatric Surgery, King Edward Memorial Hospital, Parel, Mumbai, India
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Abstract

Mesenchymal hamartoma of the liver is the second most common benign liver tumor in children, yet its biology and pathogenesis are poorly understood. Typically, it presents as a large benign multicystic liver mass in children younger than three years, amenable to complete resection. Most tumors gradually increase in size, some reaching enormous proportions, some can undergo incomplete spontaneous regression, and rarely, few have shown malignant transformation to undifferentiated (embryonal) sarcoma. Here, we report a 13 month-old child who presented with abdominal distension and respiratory distress. Ultrasonography, Computed Tomography (CT), and magnetic resonance imaging (MRI) of the abdomen were suggestive of a mesenchymal hamartoma of the liver. Right hepatectomy was performed. Postoperatively, the patient recovered well. An attempt was also made to understand the possible etiology of the tumor.

Keywords

Hemangio-endothelioma - mesenchymal hamartoma - right hepatectomy


Publication History

Article published online:
19 November 2021

© 2009. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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