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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2017; 38(01): 70-72
DOI: 10.4103/0971-5851.203515
Practitioner Section

A Case Report of Pleuropulmonary Blastoma Presenting as Tension Pneumothorax

Archana Addanki
Department of Pediatric Hemato-oncology, Aditya Birla Memorial Hospital, Pune, Maharashtra
,
Krishna Chaitanya
Department of Pediatric Hemato-oncology, Aditya Birla Memorial Hospital, Pune, Maharashtra
,
Sandip Bartakke
Department of Pediatric Hemato-oncology, Aditya Birla Memorial Hospital, Pune, Maharashtra
,
Srividya Sethuratnam
Department of Pediatric Hemato-oncology, Aditya Birla Memorial Hospital, Pune, Maharashtra
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Pleuropulmonary blastoma (PPB) is a very rare, highly aggressive, and malignant tumor that originates from either lungs or pleura. It occurs mainly in children aged <5 or 6 years. It has poor prognosis with three different subtypes: cystic (type I), combined cystic and solid (type II), and solid (type III). PPB is treated with aggressive multimodal therapies including surgery and chemotherapy. We present a case of PPB in a 3-year-old girl who presented with tension pneumothorax.

Keywords

Pleuropulmonary blastoma - primary pulmonary tumor - tension pneumothorax


Publication History

Article published online:
06 July 2021

© 2017. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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