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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2017; 38(01): 59-61
DOI: 10.4103/0971-5851.203503
Case Report

Pheochromocytoma in a Child without Hypertension: A Contribution to the “Rule of 10s”

Prasanta Kumar Tripathy
Department of Pediatric Surgery, SCB Medical College, Cuttack, Odisha, India
,
Kaumudee Pattnaik
Department of Pathology, SCB Medical College, Cuttack, Odisha, India
,
Manjushree Nayak
Department of Pathology, SCB Medical College, Cuttack, Odisha, India
,
Hiranya Kishor Mohanty
Department of Pediatric Surgery, SCB Medical College, Cuttack, Odisha, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Pheochromocytoma (PCC) is a neuroendocrine tumor originating from chromaffin tissue in adrenal medulla. Its diagnosis and treatment are well defined in adults, but experience in children is limited. Children constitute only 10% of reported cases, the average age at presentation being 11 years. The most common presentation is sustained hypertension, which is absent in only 10% of children. We managed a 14-month-old female child with PCC, but she was not hypertensive. We report two unusual features, in this case, an extremely young age at presentation and a childhood case of nonhypertensive PCC contributing for “rule of 10s.”

Keywords

Adrenal medulla - chromaffin cells - paraganglioma - pheochromocytoma


Publication History

Article published online:
06 July 2021

© 2017. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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