Abstract
Hepatic adenoma is a well-defined, benign, solitary tumor of the liver. In individuals
with glycogen storage disease I, adenoma tends to occur at a relatively younger age
and can be multiple (adenomatosis). Imaging plays a pivotal role in diagnosing hepatic
adenoma and in differentiating adenoma from other focal hepatic lesions. Especially
in patients with von Gierke disease, in addition to the associated hepatomegaly caused
by steatohepatitis and the diffusely reduced attenuation of the liver parenchyma seen
on CT, there may be more than one hepatic adenoma in up to 40% of patients. Malignant
degeneration of hepatic adenoma into hepatocellular carcinoma can occur and hence
imaging is important for prompt diagnosis of adenoma and its complications. In this
case report, we present a case of liver adenoma diagnosed by CT scan in a patient
with von Gierke disease.
Keywords
CT - Hepatic adenoma - von Gierke disease
