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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2010; 20(01): 72-74
DOI: 10.4103/0971-3026.59761
Gentiourinary Imaging

Persistent mullerian duct syndrome

Divya Renu
Department of Radiodiagnosis, RAGAVS Diagnostic and Research Centre Pvt Ltd, Sadguru Complex, No.14, 27th Cross, 4th Block West, Jayanagar, Bangalore - 560 011, India
,
B Ganesh Rao
Department of Radiodiagnosis, RAGAVS Diagnostic and Research Centre Pvt Ltd, Sadguru Complex, No.14, 27th Cross, 4th Block West, Jayanagar, Bangalore - 560 011, India
,
K Ranganath
Department of Radiodiagnosis, RAGAVS Diagnostic and Research Centre Pvt Ltd, Sadguru Complex, No.14, 27th Cross, 4th Block West, Jayanagar, Bangalore - 560 011, India
,
Namitha › Author Affiliations
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Abstract

Persistent Mullerian duct syndrome (PMDS) is a rare form of internal male pseudohermaphroditism in which Mullerian duct derivatives are seen in a male patient. This syndrome is characterized by the persistence of Mullerian duct derivatives (i.e. uterus, cervix, fallopian tubes and upper two thirds of vagina) in a phenotypically and karyotypically male patient. In this article we present the USG and MRI features of a case of PMDS with bilateral cryptorchidism and left sided inguinal hernia, containing the uterus and fallopian tubes.

Keywords

Cryptorchidism - inguinal hernia - mullerian inhibiting factor - MRI - mullerian duct derivatives - pseudohermaphroditism - USG


Publication History

Article published online:
02 August 2021

© 2010. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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