The Abernethy malformation-myriad imaging manifestations of a single entity

Samarjit S Ghuman; Saumya Gupta; T B S Buxi; Kishan S Rawat; Anurag Yadav; Naimish Mehta; Seema Sud

doi:10.4103/0971-3026.190420

Indian Journal of Radiology and Imaging, Table of Contents

CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2016; 26(03): 364-372
DOI: 10.4103/0971-3026.190420

Pediatric

The Abernethy malformation-myriad imaging manifestations of a single entity

Samarjit S Ghuman

Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

,

Saumya Gupta

Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

,

T B S Buxi

Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

,

Kishan S Rawat

Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

,

Anurag Yadav

Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

,

Naimish Mehta

Department of Surgical Gastroenterology, Sir Gangaram Hospital, New Delhi, India

,

Seema Sud

Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

› Author Affiliations

Abstract

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Abstract

Abernethy malformation, also known as congenital extrahepatic portosystemic shunts (CEPS) is a rare clinical entity and manifests with different clinical symptoms. CEPS are abnormalities of vascular development where there is shunting of portal blood into the systemic venous system. Multidetector computed tomography (MDCT) is a fast and effective modality for evaluation of CEPS. CT displays all the information desired by the surgeon as well as the clinician including the anatomy of the splenic and superior mesenteric veins, size and site of the shunt, presence or absence of the portal vein radicles, and helps to plan the therapy and even the follow-up of these patients. Contrast-enhanced magnetic resonance imaging (MRI) has also emerged as a promising tool for the evaluation of liver lesions associated with the malformation. The Radiologist should be aware of the various imaging appearances of this entity including its complications. In this article, we describe the imaging appearances of CEPS, their complications, and their imaging appearances on CT and MRI. We have also described various associated anomalies.

Keywords

Abernethy malformation - congenital extrahepatic portosystemic shunts - portosystemic shunts

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References

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