Journal of Pediatric Neuroradiology 2013; 02(02): 149-151
DOI: 10.3233/PNR-13057
Case Report
Georg Thieme Verlag KG Stuttgart – New York

Pediatric spinal adrenocortical carcinoma

Jeffrey Rykken
a   Department of Radiology, University of Minnesota, Minneapolis, MN, USA
,
Peter Kalina
b   Department of Radiology, Mayo Clinic, Rochester, MN, USA
› Author Affiliations

Subject Editor:
Further Information

Publication History

16 September 2011

01 February 2012

Publication Date:
29 July 2015 (online)

Abstract

A 5-month-old girl was found on magnetic resonance imaging to have a heterogeneously enhancing conus region mass. At surgery, an extramedullary, intradural mass was resected. Pathology confirmed a diagnosis of adrenocortical carcinoma. The neoplasm originated from ectopic adrenal cortical cell rests in the spine. Ectopic adrenal cortical tissue in the spinal canal is extremely rare. This is only the ninth reported case of an adrenocortical neoplasm arising as a primary tumor in the central nervous system.