Pulmonary artery sling is a rare congenital condition often associated with congenital
tracheal stenosis. Untreated pulmonary sling carries a high morbidity and mortality,
most of which is due to the airway and other associated anomalies rather than the
aberrant artery itself. We report the case of an infant presenting progressive respiratory
distress after a viral infection. The workup revealed a left pulmonary sling with
concomitant tracheal stenosis. This anomaly was successfully corrected by slide tracheoplasty
and left pulmonary artery reinsertion. Conclusion pulmonary artery sling is a rare entity with a nonspecific clinical presentation, a high degree of clinical
suspicion is needed in order to obtain the correct diagnosis.
Keywords
Pulmonary artery sling - stridor - respiratory failure - slide tracheoplasty
