Abstract
Posterior reversible encephalopathy syndrome (PRES) can develop in association with
a vast array of conditions including hypertensive encephalopathy and exposure to toxic
agents. Clinical manifestations include seizures, headache, focal neurological deficits,
visual disturbances and altered mental status and reversible radiological findings
such as grey and white matter abnormalities on magnetic resonance imaging. Recurrent
PRES in conjunction with periodic lateralized epileptiform discharges on electroencephalogram
has been associated with new-onset epilepsy. Here, we report a pediatric case with
systemic juvenile idiopathic arthritis with recurrent episodes of PRES and focal occipital
epilepsy. The reason for presenting this case is to show an atypical evolution of
this disease, rarely described in children.
Keywords
PRES - recurrent - epilepsy - prognosis - pediatric
