Arquivos Internacionais de Otorrinolaringologia 2010; 14(04): 481-484
DOI: 10.1590/S1809-48722010000400018
Case Report
Thieme Publicações Ltda Rio de Janeiro, Brazil

Bilateral Choanal Atresia in 34 Year-old Patients

Atresia Coanal Bilateral em Paciente de 34 Anos
Paulo Tinoco
*   Specialist in Otorhinolaryngology. Service Coordinator of Medical Residence in Otorhinolaryngology, Hospital Sao Jose do Avai.
,
José Carlos Oliveira Pereira
*   Specialist in Otorhinolaryngology. Service Coordinator of Medical Residence in Otorhinolaryngology, Hospital Sao Jose do Avai.
,
Rodolfo Caldas Lourenço Filho
*   Specialist in Otorhinolaryngology. Service Coordinator of Medical Residence in Otorhinolaryngology, Hospital Sao Jose do Avai.
,
Thiego Silveira Cajubá Brito
*   Specialist in Otorhinolaryngology. Service Coordinator of Medical Residence in Otorhinolaryngology, Hospital Sao Jose do Avai.
,
Betina Mameri Pereira
*   Specialist in Otorhinolaryngology. Service Coordinator of Medical Residence in Otorhinolaryngology, Hospital Sao Jose do Avai.
,
Vânia Lúcia Carrara
*   Specialist in Otorhinolaryngology. Service Coordinator of Medical Residence in Otorhinolaryngology, Hospital Sao Jose do Avai.
,
Sueliana Marta F. Godoy
*   Specialist in Otorhinolaryngology. Service Coordinator of Medical Residence in Otorhinolaryngology, Hospital Sao Jose do Avai.
› Author Affiliations
Further Information

Publication History

21 May 2009

07 August 2009

Publication Date:
12 February 2014 (online)

Summary

Introduction: Choanal atresia (CA) can be defined as a failure to develop the communication between the nasal cavity and nasopharynx. May occur as a plate osteo-membranous, bony or membranous. Diagnosis depends on high clinical suspicion and laboratory tests, treatment is surgical.

Objective: To report a case of an adult patient diagnosed with bilateral choanal atresia and underwent surgery.

Case Report: MLSM, 34 years old female with a history of bilateral nasal obstruction, rhinorrhea hyaline since childhood. On nasal endoscopy and CT scan of the sinuses showed bilateral membranous atresia osteo. Patient underwent endoscopic transnasal route, with production of mucosal flap covering the wound, without stent placement. Tomography was performed which showed control choanae open and broad. The patient progressed well and has normal nasal breathing.

Conclusion: AC bilateral, although rare, can occur in adult patients.

Resumo

Introdução: A atresia de coanas (AC) pode ser definida como a falha no desenvolvimento da comunicação entre a cavidade nasal e a nasofaringe. Pode ocorrer como uma placa ósteo-membranosa, óssea ou membranosa. O diagnóstico depende de alto grau de suspeição clínica e exames complementares, o tratamento é cirúrgico.

Objetivo: Relatar um caso de uma paciente adulta com diagnóstico de atresia coanal bilateral e que foi submetida a tratamento cirúrgico.

Relato do Caso: MLSM, 34 anos,sexo feminino, com história de obstrução nasal bilateral, rinorreia hialina desde a infância. Na endoscopia nasal e Tomografia Computadorizada de seios da face evidenciou atresia ósteo-membranosa bilateral. Paciente foi submetida a tratamento cirúrgico endoscópico via transnasal, com confecção de retalho mucoso cobrindo a área cruenta, sem colocação de stent. Foi feito Tomografia de controle que evidenciou coanas abertas e amplas. Paciente evoluiu bem e apresenta respiração nasal normal.

Comentários Finais: A AC bilateral, embora rara, pode ocorrer em pacientes adultos.

 
  • Bibliographic References

  • 1 Lazar RH, Younes RT. Transnasal repair of choanal atresia using telescopes. Arch Otolaryngol Head Neck Surg 1995; 121 (5) 517-20
  • 2 Schwartz ML, Savetsky L. Choanal atresia: clinical features, surgical approach, and long-term follow-up. Laryngoscope 1986; 96: 1335-9
  • 3 Keller JL, Kacker A. Choanal atresia, charge association, and congenital nasal stenosis. Otolaryngol Clin North Am 2000; 33 (6) 1343-51
  • 4 Tellier AL, Daire VC, Abadie V, Amiel JN, Sigaudy S, Bonnet D, Debeney PL, Durand MPM, Hubert P, Michel JL, Jan D, Dollfus H, Baumann C, Labrune P, Lacombe D, Philip N, Lemerrer M, Briard ML, Munnich A, Lyonnet S. Charge Syndrome: Report of 47 Cases and Review. Am Med Genet 1998; 76 (5) 402-9
  • 5 Lorens DC, Casasús JC. Atresia bilateral, ósea, de coanas en adulto. An Otorrinolaringol Ibero Am 1994; 21 (5) 487-96
  • 6 Park AH, Brockenbrough J, Stankiewicz J. Endoscopic versus traditional approaches to choanal atresia. Otolaryngol Clin North Am 2000; 33 (1) 77-90
  • 7 Samadi DS, Shah UK, Handler SD. Choanal atresia: A twenty-year review of medical comorbiditied and surgical outcomes. Laryngoscope 2003; 113: 254-8
  • 8 Schweinfurth JM. Image guidance-assisted repair of bilateral choanal atresia. Laryngoscope 2002; 112: 2096-8
  • 9 Vogels RL, Chung D, Lessa MM, Lorenzetti FTM, Goto EY, Butugan O. Bilateral congenital choanal atresia in a 13-year-old patient. Int J Pediatr Otorhinolaryngol 2002; 65: 53-7
  • 10 Josephson GD, Vickery CL, Giles WC, Gross CW. Transnasal endoscopic repair of congenital choanal atresia. Arch Otolaryngol Head Neck Surg 1998; 124 (5) 537-40
  • 11 Cedin AC, Rocha JrFP, Deppermann MB, Manzano PAM, Murao M, Shimuta AS. Transnasal endoscopic surgery of choanal atresia without the use of stents. Laryngoscope 2002; 112 (4) 750-52