Arquivos Internacionais de Otorrinolaringologia 2010; 14(04): 477-480
DOI: 10.1590/S1809-48722010000400017
Case Report
Thieme Publicações Ltda Rio de Janeiro, Brazil

Endoscopic Escalated Resection to Extensive Amyloidosis of the Upper Aero-digestive Tract: a Feasible and Effective Alternative

Ressecção Endoscópica Escalonada para Amiloidose Extensa do Trato Aéreo-digestivo Superior: Uma Alternativa Eficaz e Viável
Thiago Chianca Ferreira
*   Graduation. Resident.
,
Carlos Eduardo Fernandes Soares de Melo
*   Graduation. Resident.
,
Fernando Martinez Belentani
**   ENT. Former Resident.
,
Mayko Soares Maia
*   Graduation. Resident.
,
Romualdo Suzano Louzeiro Tiago
***   Doctor of Science at the Graduate Program in Otolaryngology and Head and Neck Surgery, UNIFESP. Attending Physician.
› Author Affiliations
Further Information

Publication History

12 May 2009

27 July 2009

Publication Date:
12 February 2014 (online)

Summary

Introduction: Localized amyloidosis is a rare disease characterized by extracellular deposition of proteins that can occur in various regions of the body. The larynx is the most common site of disease in head and neck.

Objective: We present a literature review and the case of a patient with extensive amyloidosis in the upper aero-digestive tract, whose resection was performed in four steps.

Case Report: SMS, 28 years, 4 months ago dysphonia. Complementary exams showed large lesions in supraglottic that was removed in four stages by microlaryngoscopy.

Final Comments: microlaryngoscopy tiered approach was effective and safe resection of lesions in amyloidosis large.

Resumo

Introdução: A amiloidose localizada é uma doença rara, caracterizada pelo depósito extracelular de proteínas que pode ocorrer em várias regiões do corpo. A laringe é o sítio mais comum da doença na região de cabeça e pescoço.

Objetivo: Apresentaremos uma revisão literária e o caso de um paciente com amiloidose extensa em trato aéreo-digestivo superior, cuja ressecção foi realizada em quatro etapas.

Relato do Caso: SMS, 28 anos, disfonia há 4 meses. Exames complementares evidenciaram lesão de grande dimensão em supraglote que foi ressecada em quatro etapas por microlaringoscopia.

Comentários Finais: A abordagem por microlaringoscopia escalonada mostrou-se eficaz e segura na ressecção de lesão por amiloidose de grande dimensão.

 
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