Giant Mass due to Castleman's Disease Causing Superior Vena Cava Syndrome

Introduction

Castleman's disease (CD) is a usually benign lymphoid tumor of uncertain etiology. CD was first described in 1956. It is also known as angiofollicular lymphoid hyperplasia, giant lymph node hyperplasia, lymph nodal hamartoma or benign giant lymphoma. CD generally appears as a solitary mediastinal mass [[1]]. It is usually asymptomatic and rarely presents as superior vena cava syndrome. Surgical excision in localized disease is curative [[2]]. We describe a case of mediastinal Castleman's disease which presented with vena cava superior syndrome.

References

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