Malignant Peripheral Nerve Sheath Tumor of the Orbit: Case Report and Literature Review

Mehmet D. Aydin; Umran Yildirim; Cemal Gundogdu; Osman Dursun; Hasan H. Uysal; Mete Ozdikici

doi:10.1055/s-2004-828705

Skull Base, Table of Contents

Skull Base 2004; 14(2): 109-113
DOI: 10.1055/s-2004-828705

CASE REPORT

Malignant Peripheral Nerve Sheath Tumor of the Orbit: Case Report and Literature Review

Mehmet D. Aydin¹ , Umran Yildirim² , Cemal Gundogdu² , Osman Dursun³ , Hasan H. Uysal³ , Mete Ozdikici⁴

¹Department of Neurosurgery, Medical Faculty, Ataturk University, Erzurum, Turkey
²Department of Pathology, Medical Faculty, Ataturk University, Erzurum, Turkey
³Department of Ophthalmology, Social Security Hospital, Erzurum, Turkey
⁴Department of Radiology, Erzurum State Hospital, Erzurum, Turkey

Abstract

A 68-year-old woman with progressive visual loss and exophthalmos in her right eye had been operated on for a mass in her right calf 3 years earlier. Imaging showed a huge mass invading the orbital structures and temporal pole. The presumptive diagnosis was a malignant orbital tumor. The tumor was resected totally and eroded tissues such as the lateral rectus muscle and dural compartments were repaired. The histological diagnosis was a malignant peripheral nerve sheath tumor (MPNST). The patient recovered uneventfully and was discharged 8 days after surgery. Two years later she died from a liver tumor. Few MPNSTs involving the orbit have been reported.

KEYWORDS

Malignant peripheral nerve sheath tumor - orbit

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References

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Dr
Mehmet D Aydin

Atatürk Üniversitesi Lojmanlari

60 Blok, Kat 1, No. 3, Erzurum, Turkey

Email: nmda21@hotmail.com