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Semin Hear 2003; 24(3): 179-188
DOI: 10.1055/s-2003-41217
Copyright © 2002 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA. Tel.: +1(212) 584-4662

Evaluation of Neurologic Syndromes with Mental Retardation and Auditory Sequelae

Glenn Edward Green
  • Department of Surgery, Pediatrics, and Speech & Hearing Sciences, University of Arizona, Tucson, Arizona
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Publication History

Publication Date:
14 August 2003 (online)

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ABSTRACT

When the audiological function of a mentally retarded person is being assessed, knowledge of the etiology of the mental retardation and its associated findings can be used to optimize testing. This is particularly important when the ability of the patient to tolerate comprehensive testing is limited. Mental retardation has hundreds of different causes, many of which have associated hearing loss or deafness as a syndrome. Still, even when a specific syndrome has not been identified, audiological testing may be tailored to differentiate causes of mental retardation and to guide evaluation and treatment. Several representative syndromes and their corresponding audiological findings are described to illustrate the role of audiological assessment in the overall care of the patient with syndromal mental retardation. Resources are provided to help the reader locate corresponding information for other syndromes. Through the use of this knowledge, the care of the mentally retarded can be improved.

KEYWORDS

Hearing loss - mental retardation - syndromes

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