Zusammenfassung
Es wird über den Fall eines Karpaltunnelsyndroms bei einem 12-jährigen Mädchen mit
Klippel-Trénaunay-Syndrom berichtet. Im Karpalkanal und in der Hohlhand findet sich
ein kavernöses Hämangiom, das außer durch mechanische Kompression wohl auch durch
die veränderte Hämodynamik zur ischämischen Schädigung des N. medianus führt.
Summary
The case of a 12-year-old girl with Klippel-Trénaunay syndrome and the signs of median
nerve entrapment is reported. A cavernous haemangioma surrounding the median nerve
is thought to be responsible for the carpal tunnel syndrome through mechanical compression
and ischemic damage to the nerve due to the changed haemodynamic situation in the
carpus.
Schlüsselwörter
Angeborene Fehlbildungen - Klippel-Trénaunay-Syndrom - Nervenkompressionssyndrom:
N. medianus - Karpaltunnelsyndrom beim Kind - kavernöses Hämangiom
Key words
Congenital malformations - Klippel-Trénaunay syndrome - nerve compression syndrome:
median nerve - carpal tunnel syndrome in the child - cavernous haemangioma
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Dr. med. Mark Mettler
Regionales Spitalzentrum RSZ
Abteilung Chirurgie
3110 Münsingen
Schweiz
