Zusammenfassung
Die gebräuchlichen Klassifikationen der Choledochuszyste wurden überwiegend aus Befunden,
die an Erwachsenen erhoben worden waren, abgeleitet. Die Kombination mit einer Gallengangsatresie,
die bei ca. 6 % aller Choledochuszysten vorkommt, ist nicht extra klassifiziert. Diese
Kombination weist jedoch sowohl von der Genese als auch der Dringlichkeit her bezüglich
Diagnostik und Therapie Besonderheiten auf, die eine extra Klassifikation erfordern.
Classification of choledochal cysts associated with extrahepatic biliary atresia
Summary
The most widely used classifications of choledochal cysts have been derived mainly
from findings in adult patients. The association of congenital biliary dilatation
with biliary atresia is not classified as a special group or subgroup. There are several
reasons, however, to classify this association as an extra group: It is a separate
etiologic entity; early detection of this rare disorder is important and surgical
correction is urgent to prevent biliary cirrhosis.
Schlüsselwörter
Choledochuszyste - Klassifikation - Gallengangsatresie
Key words
Choledochal cyst - biliary atresia - classification
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1 * Vorgetragen auf der Jahrestagung der Deutschen Gesellschaft für Kinderchirurgie,
München 9.-12. 9. 1999
Korrespondenzadresse:Prof. Dr. Klaus Heller
Funktionsbereich KinderchirurgieKlinik für Allgemein- und GefäßchirurgieKlinikum der
J.W. Goethe-Universität
Th. Stern-Kai 7
D-60590 Frankfurt am Main
Telefon: Tel.: 0 69/63 01-66 59
Fax: Fax: 0 69/63 01-79 36
eMail: E-mail: kheller@zki.uni-frankfurt.de