CC BY-NC-ND 4.0 · Arquivos Brasileiros de Neurocirurgia: Brazilian Neurosurgery 2025; 44(01): e56-e58
DOI: 10.1055/s-0045-1805011
Case Report

Orbital Pseudotumor: Neurosurgical Perspective

Pseudotumor orbitário: Perspectiva neurocirúrgica
1   Department of Neurosurgery, School of Medicine, Universidade Estadual de Ponta Grossa, PR, Brazil
,
Giovana S. Ceconello
2   School of Medicine, Universidade Federal do Mato Grosso do Sul, MS, Brazil
,
Leonardo C. Welling
3   Department of Neurosurgery, School of Medicine, Universidade Estadual de Ponta Grossa, PR, Brazil
› Institutsangaben

Abstract

Idiopathic orbital inflammation is the third most common orbital affection, characterized by a benign inflammatory process, which is neither infectious nor neoplastic and can affect any orbital tissue. A 31-year-old female patient was referred to neurosurgical evaluation due to left orbital pseudotumor, which was nonresponsive to high doses of corticosteroid therapy. During the neurological examination, we identified reduced visual acuity, complete external ophthalmoplegia, ocular pain, and severe proptosis. A neurosurgical intervention with lateral orbitotomy was performed, with great pain relief. In the present case report, we discuss the disease and its natural course and call the attention of neurosurgeons to prompt intervention in selected cases.

Resumo

A inflamação orbital idiopática é a terceira causa mais comum de afecção orbital, caracterizada por processo inflamatório benigno, não infeccioso nem neoplásico, o qual pode acometer qualquer tecido orbital. Uma paciente de 31 anos, foi encaminhada para neurocirurgia em decorrência de um pseudotumor orbital à esquerda, o qual não respondeu ao tratamento com altas doses de corticosteroides. No exame neurológico, foram identificadas redução da acuidade visual, oftalmoplegia externa, dor ocular e ptose severa. Neste relato de caso, discutimos o curso natural da doença e chamamos a atenção dos neurocirurgiões para a intervenção de urgência em casos selecionados.



Publikationsverlauf

Eingereicht: 30. Mai 2023

Angenommen: 23. Oktober 2024

Artikel online veröffentlicht:
27. März 2025

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