Overcoming Complexity: Percutaneous Embolization for Hepatic Artery Pseudoaneurysms in Hereditary Hemorrhagic Telangiectasia (HHT)

Abstract

Osler-Weber-Rendu syndrome also known as hereditary hemorrhagic telangiectasia (HHT) is a rare vascular dysplasia affecting multiple organ systems in the body. Hepatic manifestations of HHT include telangiectasias, large confluent masses, hepatic perfusion abnormalities, and various types of intrahepatic vascular shunts. Spontaneous hepatic pseudoaneurysm (PA) in HHT is a less well-known phenomenon, with fewer than 20 cases reported in the literature so far. Even rarer is the use of percutaneous glue (N-butyl cyanoacrylate) embolization to manage multiple hepatic PAs in HHT syndrome. The purpose of this case report is to describe the successful management of multiple hepatic PAs by percutaneous embolization in a 56-year-old male diagnosed with HHT.

Keywords

hereditary hemorrhagic telangiectasia - pseudoaneurysms - glue embolization

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