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CC BY-NC-ND 4.0 · Indian J Radiol Imaging
DOI: 10.1055/s-0045-1805005
Case Report

Overcoming Complexity: Percutaneous Embolization for Hepatic Artery Pseudoaneurysms in Hereditary Hemorrhagic Telangiectasia (HHT)

Anjali Sah
1   Department of Radio-diagnosis & Interventional Radiology, All India Institute of Medical Sciences, New Delhi, India
,
Rajendra Kumar Behera
1   Department of Radio-diagnosis & Interventional Radiology, All India Institute of Medical Sciences, New Delhi, India
,
Anuradha Sharma
1   Department of Radio-diagnosis & Interventional Radiology, All India Institute of Medical Sciences, New Delhi, India
,
Shivanand Gamanagatti 
1   Department of Radio-diagnosis & Interventional Radiology, All India Institute of Medical Sciences, New Delhi, India
,
Ayush Agarwal
2   Department of Gastroenterology and Human Nutrition, All India Institute of Medical Sciences, New Delhi, India
,
Soumya Jagannath Mahapatra
2   Department of Gastroenterology and Human Nutrition, All India Institute of Medical Sciences, New Delhi, India
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Abstract

Osler-Weber-Rendu syndrome also known as hereditary hemorrhagic telangiectasia (HHT) is a rare vascular dysplasia affecting multiple organ systems in the body. Hepatic manifestations of HHT include telangiectasias, large confluent masses, hepatic perfusion abnormalities, and various types of intrahepatic vascular shunts. Spontaneous hepatic pseudoaneurysm (PA) in HHT is a less well-known phenomenon, with fewer than 20 cases reported in the literature so far. Even rarer is the use of percutaneous glue (N-butyl cyanoacrylate) embolization to manage multiple hepatic PAs in HHT syndrome. The purpose of this case report is to describe the successful management of multiple hepatic PAs by percutaneous embolization in a 56-year-old male diagnosed with HHT.

Keywords

hereditary hemorrhagic telangiectasia - pseudoaneurysms - glue embolization


Publication History

Article published online:
27 March 2025

© 2025. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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