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J Neurol Surg A Cent Eur Neurosurg 2025; 86(03): 327-330
DOI: 10.1055/s-0044-1791974
Case Report

Intraorbital Retrobulbar Salivary Gland Choristoma: Presentation of a Unique Case and Review of the Literature

Leonard Ritter 
1   Department of Neurosurgery, Klinikum Nürnberg, Paracelsus Medical University, Nuremberg, Germany
,
Thomas Eibl
1   Department of Neurosurgery, Klinikum Nürnberg, Paracelsus Medical University, Nuremberg, Germany
,
Adrian Liebert
1   Department of Neurosurgery, Klinikum Nürnberg, Paracelsus Medical University, Nuremberg, Germany
,
Cristiane Blechschmidt
2   Institute for Pathology, Klinikum Nürnberg, Paracelsus Medical University, Nurnberg, Bayern, Germany
,
Maximilian Traxdorf
3   Department of Otorhinolaryngology, Klinikum Nürnberg, Paracelsus Medical University, Nurnberg, Bayern, Germany
,
Karl-Michael Schebesch
1   Department of Neurosurgery, Klinikum Nürnberg, Paracelsus Medical University, Nuremberg, Germany
› Author Affiliations Funding None.
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Abstract

Background A choristoma is defined as the accumulation of normal tissue in an abnormal location. Salivary gland choristomas are a rare entity that is most frequently described in the middle ear. However, there are a few reported cases of salivary gland choristomas in other locations like the pituitary gland and the optic nerve dural sheath. To the best of our knowledge, we present the first case of a patient with an intraconal salivary gland choristoma. A brief but comprehensive review of literature is offered, additionally.

Methods A 19-year-old male patient presented with disturbance of ocular motility, ptosis, and exophthalmos of the right eye. The subsequent imaging by magnetic resonance imaging (MRI) demonstrated an intraconal lesion that infiltrated the lateral and medial rectal muscles of the right eye. The lesion showed intensive gadolinium enhancement in T1-weighted sequence and the fluid-attenuated inversion recovery (FLAIR) sequence showed no intracranial edema. The interdisciplinary neuro-oncologic tumor board recommended a biopsy and partial removal of the lesion.

Results Partial resection of the choristoma was successfully performed via lateral orbitotomy. No new neurologic or visual deficits occurred postoperatively. During the 2-week follow-up examination, the exophthalmos had completely regressed and the patient only reported a slight retrobulbar pressure sensation. The histopathologic examination of the tissue revealed seromucous glandular tissue.

Conclusion Salivary gland choristomas have been occasionally described intracranially before, but this is the first case of an intraconal accumulation of salivary gland tissue. Partial resection was achieved, resulting in complete recovery of the ophthalmologic symptoms.

Keywords

choristoma - salivary gland - intracranial - heterotopia - skull base surgery

Ethical Approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.


Informed Consent

Informed consent was obtained from the patient described in this case report.




Publication History

Received: 20 February 2024

Accepted: 14 August 2024

Article published online:
19 November 2024

© 2024. Thieme. All rights reserved.

Georg Thieme Verlag KG
Rüdigerstraße 14, 70469 Stuttgart, Germany

 

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