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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2025; 35(02): 339-342
DOI: 10.1055/s-0044-1791672
Case Report

Persistent Levoatriocardinal Vein in Association with Complete Duplication of SVC and IVC

Arun Sharma    *
1   Department of Radiodiagnosis and Imaging, Postgraduate Institute of Medical Education and Research, Chandigarh, India
,
Pavithra Subramanian    *
1   Department of Radiodiagnosis and Imaging, Postgraduate Institute of Medical Education and Research, Chandigarh, India
,
Abhishek Mallick
2   Department of Cardiology, Postgraduate Institute of Medical Education and Research, Chandigarh, India
,
Manoj Kumar Rohit 
2   Department of Cardiology, Postgraduate Institute of Medical Education and Research, Chandigarh, India
,
Manphool Singhal 
1   Department of Radiodiagnosis and Imaging, Postgraduate Institute of Medical Education and Research, Chandigarh, India
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Abstract

Persistent levoatriocardinal vein (LACV) is a rare pulmonary venous anomaly characterized by persistence of embryonic pulmonary to systemic communication. It is commonly associated with obstructive lesions of the left heart, such as hypoplastic left heart syndrome and mitral atresia. Complete duplication of the superior vena cava (SVC) and inferior vena cava (IVC) is rare, and occurs due to aberrations in the multistep development of the cardinal venous system. Coexistence of double SVC and IVC has been reported in the literature; however, their occurrence with persistent levoatriocardinal vein is hitherto unreported. The current case describes a rare coexistence of these complex pulmonary and systemic venous anomalies: persistent levoatriocardinal vein in a child with double SVC and IVC. The embryological development and possible aberrations leading to these anomalies are also detailed.

Keywords

congenital cardiac anomaly - CT angiography - IVC duplication - levoatriocardinal vein - SVC duplication

* Contributed equally and share first authorship.


Supplementary Material



Publication History

Article published online:
24 October 2024

© 2024. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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