CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2024; 34(03): 545-548
DOI: 10.1055/s-0043-1777745
Case Report

Macrodystrophia Lipomatosa: A Rare Case of Ulnar Nerve Territory Involvement

Sonali Ullal
1   Department of Radiodiagnosis and Imaging, Kasturba Medical College, Mangalore, India
1   Department of Radiodiagnosis and Imaging, Kasturba Medical College, Mangalore, India
› Author Affiliations
Funding None.


Macrodystrophia lipomatosa (MDL) is a rare congenital, nonhereditary anomaly characterized by overgrowth of all the mesenchymal elements, predominantly the fibroadipose tissue in a sclerotomal distribution commonly involving the median nerve territory in the upper extremity and plantar nerve territory in the lower extremity. It can be either static or progressive, with the former being the more common. MDL is usually present since birth and the affected digit/region increases in length and girth, and growth ceases after puberty. We discuss a rare case of ulnar nerve territory involvement that progressed to grow even after puberty.

Publication History

Article published online:
28 December 2023

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