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CC BY-NC-ND 4.0 · Arquivos Brasileiros de Neurocirurgia: Brazilian Neurosurgery 2024; 43(01): e69-e72
DOI: 10.1055/s-0043-1776266
Case Report

Cobb Syndrome Associated with Spinal Cavernoma – Case Report

Síndrome de Cobb associada a cavernoma medular – Relato de caso
Paulo Moacir Mesquita Filho
1   Neurosurgery Department, Hospital de Clínicas de Passo Fundo, Passo Fundo, RS, Brazil
2   Liga Acadêmica do Serviço de Neurologia e Neurocirurgia, Passo Fundo, RS, Brazil
,
Luan Lucena
1   Neurosurgery Department, Hospital de Clínicas de Passo Fundo, Passo Fundo, RS, Brazil
,
Leticia Bassani Devens
2   Liga Acadêmica do Serviço de Neurologia e Neurocirurgia, Passo Fundo, RS, Brazil
,
Luana Rossato Dias 
2   Liga Acadêmica do Serviço de Neurologia e Neurocirurgia, Passo Fundo, RS, Brazil
,
Bruno Missio Gregol
2   Liga Acadêmica do Serviço de Neurologia e Neurocirurgia, Passo Fundo, RS, Brazil
,
Nério Dutra Azambuja Jr
1   Neurosurgery Department, Hospital de Clínicas de Passo Fundo, Passo Fundo, RS, Brazil
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Abstract

Cobb syndrome, or cutaneomeningospinal angiomatosis, is a rare condition that affects young adults, and its etiology has not been completely elucidated. It is characterized by a cutaneous sign, or stigma, associated with spinal or intracranial malformations. The symptoms are quite diverse, but, in most cases, the disease presents motor deficit and pain. The present study reports the case of a 48-year-old female patient, who initially sought dermatological medical care for a single skin lesion in the posterior cervical region. During the excision, it was noticed that the lesion had contiguous behavior to the deep anatomical planes, thus requiring the evaluation of the neurosurgical team. The purpose of this report is to describe this rare disease, covering more details about diagnosis and therapy.

Resumo

Síndrome de Cobb, ou angiomatose cutâneo-meningo-espinhal, é uma condição rara que afeta adultos jovens, e sua etiologia não foi completamente elucidada. Caracteriza-se por um sinal cutâneo, ou estigma, associado a malformações espinhais ou intracranianas. Os sintomas são bastante diversos, mas, na maioria dos casos, a doença apresenta déficit motor e dor. O presente estudo relata o caso de uma paciente do sexo feminino de 48 anos, que inicialmente procurou atendimento médico dermatológico para uma única lesão cutânea na região cervical posterior. Durante a excisão, notou-se que a lesão apresentava comportamento contíguo aos planos anatômicos profundos, exigindo assim a avaliação da equipe neurocirúrgica. O objetivo deste relatório é descrever essa doença rara, abrangendo mais detalhes sobre diagnóstico e terapia.

Keywords

arteriovenous malformation - nevus - angiomatosis - Cobb syndrome

Palavras-chave

malformação arteriovenosa - nevo - angiomatose - Síndrome de Cobb


Publication History

Received: 17 December 2020

Accepted: 22 February 2021

Article published online:
31 October 2023

© 2023. Sociedade Brasileira de Neurocirurgia. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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