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CC BY-NC-ND 4.0 · Asian J Neurosurg
DOI: 10.1055/s-0043-1772764
Case Report

Primary Extraskeletal Falcine Myxoid Chondrosarcoma—A Case Report and Review of Literature

Rajasekhar Narayanan
1   Department of Neurosurgery, Ananthapuri Hospitals and Research Institute, Thiruvananthapuram, Kerala, India
,
Renjith T. Venugopal
1   Department of Neurosurgery, Ananthapuri Hospitals and Research Institute, Thiruvananthapuram, Kerala, India
,
Suresh Kumar K. L.
1   Department of Neurosurgery, Ananthapuri Hospitals and Research Institute, Thiruvananthapuram, Kerala, India
,
Jose P. B.
1   Department of Neurosurgery, Ananthapuri Hospitals and Research Institute, Thiruvananthapuram, Kerala, India
,
Anjana Bahuleyan
2   Department of Pathology, Ananthapuri Hospitals and Research Institute, Thiruvananthapuram, Kerala, India
,
Reshmi C. P.
3   Department of Radiodiagnosis, Ananthapuri Hospitals and Research Institute, Thiruvananthapuram, Kerala, India
,
Thomas Varghese
1   Department of Neurosurgery, Ananthapuri Hospitals and Research Institute, Thiruvananthapuram, Kerala, India
,
Marthanda A. Pillai
1   Department of Neurosurgery, Ananthapuri Hospitals and Research Institute, Thiruvananthapuram, Kerala, India
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Abstract

Intracranial chondrosarcomas are rare malignant lesions. Both skull base and dural-based extraosseous chondrosarcomas have been reported to occur intracranially. Dural-based chondrosarcomas arising from the falx cerebri are rare lesions with only 19 cases reported till date. Although conventional, mesenchymal, and myxoid variants of chondrosarcomas have been reported intracranially, myxoid variant are the rarest with only 17 cases reported till date, among which only 2 were falcine. We are reporting the third case of falcine myxoid chondrosarcoma in a 32-year-old man who presented with seizures and subtle lower limb weakness. Radiological findings were suggestive of an atypical meningioma in the falcine region. Macroscopically total resection of the tumor was done. Histopathological examination confirmed myxoid chondrosarcoma, grade 1. Postoperative period was uneventful, and the patient remains asymptomatic 34 months after the surgery without the application of any adjuvant therapy. Falcine myxoid chondrosarcomas are extremely rare lesions with variable aggressiveness as suggested by the three cases reported till now including the present case.

Keywords

chondrosarcoma - dural based - extraskeletal - falcine - intracranial - myxoid

Ethical Approval

This work has been approved by the Institutional Review Board of Ananthapuri Hospitals and Research Institute.


Authors' Contribution

All authors contributed to the study conception and design. Material preparation and data collection were performed by R.N. The final draft of the manuscript was written by R.N. and M.P.A., and all authors commented on previous versions of the manuscript. All authors read and approved the final manuscript.




Publication History

Article published online:
13 May 2024

© 2024. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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