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CC BY 4.0 · Avicenna J Med 2023; 13(01): 056-059
DOI: 10.1055/s-0043-1764376
Case Report

Idiopathic Isolated Right Ventricular Cardiomyopathy: A Rare Case Report

Vivek Mohanty
1   Department of Cardiology, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India
,
Shubham Kumar Sharma
1   Department of Cardiology, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India
,
Sourabh Goswami
1   Department of Cardiology, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India
,
Rahul Gudhage
1   Department of Cardiology, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India
,
Surender Deora 
1   Department of Cardiology, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India
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Abstract

Idiopathic isolated right ventricular cardiomyopathy is an extremely rare cause of right ventricular failure. Here, we report a case of 65-year-old male presented with chief complaints of dyspnea, fatigue, and bilateral pedal edema for the last 6 months. On clinical evaluation, grade II/III pansystolic murmur was present in left parasternal area. Investigations and imaging revealed dilated right atrium and ventricle with normal pulmonary artery pressure without any etiology. Magnetic resonance imaging ruled out other common causes of right ventricular cardiomyopathy; thus, the patient was diagnosed as a case of idiopathic isolated right ventricular cardiomyopathy that is a diagnosis of exclusion.

Keywords

idiopathic - right ventricle - cardiomyopathy

Author Contributions

V.M. and S.K.S. were involved in the diagnostic workup and collected the clinical data. S.G. and R.G. wrote the first draft and followed the patient. S.D. researched the documented cases, organized the figures and tables, and edited the manuscript. All authors reviewed and approved the final manuscript before submission.




Publication History

Article published online:
24 March 2023

© 2023. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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  • References

  • 1 Matsui S, Murakami E, Takekoshi N, Tsuji S. Idiopathic dilated right ventricular cardiomyopathy: a report of eight cases. J Cardiogr 1985; 15 (04) 1027-1038
    PubMedGoogle Scholar
  • 2 Briongos Figuero S, Acena Navarro A. Isolated right ventricular dilated cardiomyopathy: an early diagnosis. J Clin Med Res 2015; 7 (10) 817-819
    CrossrefPubMedGoogle Scholar
  • 3 Ibsen HH, Baandrup U, Simonsen EE. Familial right ventricular dilated cardiomyopathy. Br Heart J 1985; 54 (02) 156-159
    CrossrefPubMedGoogle Scholar
  • 4 Elikowski W, Małek-Elikowska M, Różańska P, Fertała N, Zawodna M. Isolated right ventricular takotsubo cardiomyopathy: a case report and literature review. Pol Merkuriusz Lek 2016; 41 (246) 283-286
    Google Scholar
  • 5 Seecheran RV, Ramdin R, Singh S. et al. Isolated right ventricular noncompaction cardiomyopathy causing pulmonary embolism. J Investig Med High Impact Case Rep 2021; 9: 23 247096211024027
    Google Scholar
  • 6 Yelve K, Panandikar GA, Pazare A, Bajpai S. Isolated right ventricular cardiomyopathy with autoimmune hypothyroidism: a rare association in an adolescent. BMJ Case Rep 2015; 2015: bcr2014206268
    Google Scholar
  • 7 Belin RJ, Varga J, Collins JD, Freed BH. Right ventricular cardiomyopathy in systemic sclerosis. Rheumatology (Oxford) 2017; 56 (06) 1045-1047
    CrossrefPubMedGoogle Scholar
  • 8 Bosman LP, Cadrin-Tourigny J, Bourfiss M. et al. Diagnosing arrhythmogenic right ventricular cardiomyopathy by 2010 Task Force Criteria: clinical performance and simplified practical implementation. Europace 2020; 22 (05) 787-796
    CrossrefPubMedGoogle Scholar
  • 9 Gomathi SB, Makadia N, Ajit SM. An unusual case of isolated non-compacted right ventricular myocardium. Eur J Echocardiogr 2008; 9 (03) 424-425
    CrossrefPubMedGoogle Scholar
  • 10 Ganczar J, English R. Uhl's anomaly: absence of the right ventricular myocardium. Ann Pediatr Cardiol 2015; 8 (01) 71-73
    CrossrefPubMedGoogle Scholar