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CC BY 4.0 · Surg J (N Y) 2022; 08(03): e266-e269
DOI: 10.1055/s-0042-1757335
Case Report

Extra-Gastrointestinal Stromal Tumor (EGIST) in the Pelvis Mimicking Retroperitoneal Sarcoma

Etienne El-Helou    *
1   Department of General Surgery, Lebanese University, Faculty of Medical Sciences, Beirut, Lebanon
,
Linda Chamma    *
1   Department of General Surgery, Lebanese University, Faculty of Medical Sciences, Beirut, Lebanon
,
Houssam Bashir Mazraani
1   Department of General Surgery, Lebanese University, Faculty of Medical Sciences, Beirut, Lebanon
,
Delivrance Sebaaly
2   Department of Anatomic Pathology, Lebanese University, Faculty of Medical Sciences, Beirut, Lebanon
,
Omar Georges Chamma 
3   Department of Internal Medicine, Lebanese University, Faculty of Medical Sciences, Beirut, Lebanon
,
Jessica Naccour 
4   Department of Emergency Medicine, Lebanese University, Faculty of Medical Sciences, Beirut, Lebanon
,
Marwan M. Haddad
5   Department of Radiology, Mount Lebanon Hospital, Beirut, Lebanon
,
Dani Lichaa
6   Department of General Surgery, Centre Hospitalier Universitaire Geitaoui, Beirut, Lebanon
,
Houssam Alam
6   Department of General Surgery, Centre Hospitalier Universitaire Geitaoui, Beirut, Lebanon
› Author Affiliations Funding This research did not receive any specific grant from funding agencies in the public, commercial, or not-for-profit sectors.
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Abstract

Extra-gastrointestinal stromal tumors (EGISTs) are rare mesenchymal tumors accounting for less than 1% of total gastrointestinal tumors. They tend to be aggressive and have a poor prognosis. Unfortunately, there is a lack of data or controversial data due to its scarcity. Therefore, we report a case of pelvic EGIST misdiagnosed as retroperitoneal sarcoma. We opted for surgical management followed by adjuvant oral chemotherapy with imatinib.

Keywords

extra-gastrointestinal - stromal tumors - GIST - retroperitoneal sarcoma - surgery - case report

* These authors contributed equally to this work.




Publication History

Received: 02 January 2022

Accepted: 07 September 2022

Article published online:
26 September 2022

© 2022. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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  • References

  • 1 Uzunoglu H, Tosun Y. Primary extra gastrointestinal stromal tumors of the abdomen. North Clin Istanb 2021; 8 (05) 464-471
    PubMedGoogle Scholar
  • 2 Elagami MM, Khalid A, Kumar V, Singhal M, Grossman MA. Perirectal extragastrointestinal stromal tumor: an unusual presentation. Cureus 2021; 13 (06) e15529 DOI: 10.7759/cureus.15529.
    CrossrefPubMedGoogle Scholar
  • 3 Kadel D, Bhuju S, Thapa BR, Chalise S, Kumar Sah S. Curative intent treatment of late presented extragastrointestinal stromal tumor: two identical case reports with literature review. J Surg Case Rep 2021; 2021 (06) rjab220 DOI: 10.1093/jscr/rjab220.
    CrossrefPubMedGoogle Scholar
  • 4 Feng H, Hu W, Zheng C. et al. Clinical features of extragastrointestinal stromal tumor compared with gastrointestinal stromal tumor: a retrospective, multicenter, real-world study. J Oncol 2021; 2021: 1460131 DOI: 10.1155/2021/1460131.
    CrossrefPubMedGoogle Scholar