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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2022; 32(03): 422-425
DOI: 10.1055/s-0042-1754316
Case Report

Trigeminal Nerve Melanotic Schwannoma in Carney Complex

Kumar G.G. Sharath 
1   Department of Diagnostic and Interventional Neuroradiology, Apollo Hospitals, Sheshadripurum, Bengaluru, Karnataka, India
,
Panduranga Shruthi
2   Department of Radiology and Imaging, Apollo Hospitals, Jayanagar, Bengaluru, Karnataka, India
,
B. Varwatte Pooja
2   Department of Radiology and Imaging, Apollo Hospitals, Jayanagar, Bengaluru, Karnataka, India
,
Mohan Rao Ravi
3   Department of Neurosurgery, Apollo Hospitals, Sheshadripuram, Bengaluru, Karnataka, India
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Abstract

Melanotic schwannoma (MS) is a rare peripheral nerve sheath tumor commonly found in the thoracic paraspinal region. It is present in an intracranial location rarely, with 18 out of 105 MS cases described in the literature. Trigeminal nerve was involved in only six of these cases. Fifty percent of psammomatous melanotic schwannoma (PMS) patients have Carney complex. Carney complex is an autosomal dominant disorder featuring peripheral nerve tumors (schwannomas), myxomas (heart, skin, and breast), skin pigmentation (lentigines and blue nevi), and endocrine tumors (adrenal, testicular, and pituitary). We present a case of left trigeminal nerve PMS as a part of Carney complex. Patient had diffuse lentiginosis. Magnetic Resonance Imaging revealed enhancing lesion along left trigeminal nerve with widened Meckel's cave and foramen ovale. Final diagnosis of PMS was derived on clinical, radiological, and histopathological findings with immunohistochemistry correlation.

Key Message

Trigeminal nerve can be rarely involved in melanotic schwannoma (MS). Knowledge of typical radiological features of MS is crucial for its diagnosis. Its association with Carney complex should be sought.

Keywords

melanotic schwannoma - psammoma bodies - intracranial - Meckel's cave - trigeminal nerve - mandibular - foramen ovale - CT - MRI

Source(s) of Support

Nil.




Publikationsverlauf

Artikel online veröffentlicht:
31. Juli 2022

© 2022. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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