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CC BY-NC-ND 4.0 · Revista Iberoamericana de Cirugía de la Mano 2022; 50(01): e43-e48
DOI: 10.1055/s-0042-1748850
Update Article | Artículo de Actualización

Congenital Radial Dysplasia

Article in several languages: English | español
Manuel Méndez Becerra
1   Orthopedics Department, Facultad de Medicina, Universidad de Chile, Santiago, Chile
2   Upper Limb Team, Instituto Teletón, Santiago, Chile
3   Hand Team, Hospital Clínico, Pontificia Universidad Católica de Chile, Santiago, Chile
,
Pamela Escalona D'Angelo
4   Occupational Therapy Unit, Instituto Teletón, Santiago, Chile
,
Magdalena Méndez Pérez
5   Pontificia Universidad Católica de Chile, Santiago, Chile
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Abstract

Radial dysplasia (RD) is a congenital condition which can affect the entire upper limb, compromising multiple tissues, and it always features alterations in the thumb. It can be uni- or bilateral condition, the latter being very disabling. Treatment with manipulations, casts and/or orthoses is recommended for the least severe presentations of this disease. The surgical treatment is reserved for the most severe cases, and carpal centralization is the treatment of choice today. The most frequent complication of this intervention is the recurrence of the deformity. The patients submitted to the surgical treatment report a significant improvement in the cosmetic aspect of the extremity. The current challenge is to improve the follow-up and the use of functional assessment tools regarding the results.

Keywords

radial dysplasia - congenital upper limb anomalies - congenital hand surgery


Publication History

Received: 25 December 2020

Accepted: 29 March 2022

Article published online:
23 June 2022

© 2022. SECMA Foundation. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commecial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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