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Homœopathic Links 2022; 35(03): 175-180
DOI: 10.1055/s-0042-1743484
Case Report

Hailey-Hailey Disease Treated with Individualised Homoeopathy—An Evidence-Based Case Report

P. Dastagiri 
1   National Homoeopathy Research Institute in Mental Health, Under Central Council for Research in Homoeopathy, Ministry of AYUSH, Kottayam, Kerala, India
,
Nirmala Pratap
1   National Homoeopathy Research Institute in Mental Health, Under Central Council for Research in Homoeopathy, Ministry of AYUSH, Kottayam, Kerala, India
› Author Affiliations Funding Nil.
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Abstract

Hailey-Hailey disease (HHD) is a rare autosomal dominant skin disorder presented as blistering dermatosis with recurrent erythematous plaques, leading to erosions, fissures and vegetations seen in the skin folds. Prevalence of this disease occurs in 1 to 4 per 100,000 affected between third and fourth decade, mostly either under-reported or misdiagnosed. Under standard conventional treatment, recurrence and remissions are typical. Therefore, it affects the quality of life compared with other skin disorders. However, with the individualised homoeopathic medicine, Psorinum, this rare case was treated without topicals; no recurrence of the complaints and adverse effects were observed in 1 year of follow-up. Furthermore, changes in the dermatology life quality of life questionnaire score from 20 (at baseline) to zero have been noticed; the modified Naranjo criteria for homeopathy total score was +9 out of +13, providing evidence attributed by the intervention. This case report reinforces that individualised homoeopathic intervention is beneficial in rare skin disorders like HHD, and pooling such data will develop future research concepts in this area.

Keywords

Hailey-Hailey disease - homoeopathy - Psorinum - dermatology life quality of life (DLQI) questionnaire - Modified Naranjo criteria for homeopathy (MONARCH)

Patient Perspective

I visited the institute with severe itching all over the body, peeling off the skin, along with constipation and sleeplessness due to unbearable itching, and consulted, consumed, much conventional medicine without any significant relief. However, after taking the treatment, I observed and felt all complaints were relieved markedly with less expenditure and no side effects.


Declaration of Patient Consent

The authors certify that they have obtained patient consent and that the patient has given his consent for his photographs and other clinical information to be reported in the journal. In addition, the patient was made to understand that his name and initials will not be published, and efforts will be made to conceal his identity.




Publication History

Article published online:
30 September 2022

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