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CC BY 4.0 · European J Pediatr Surg Rep. 2022; 10(01): e25-e29
DOI: 10.1055/s-0042-1743159
Case Report

Juvenile Xanthogranuloma as Differential Diagnosis of a Vulvar Mass: A Case Report

Isabel Bada Bosch
1   Department of Pediatric Surgery, Hospital General Universitario Gregorio Marañón, Madrid, Spain
,
Agustín del Cañizo
1   Department of Pediatric Surgery, Hospital General Universitario Gregorio Marañón, Madrid, Spain
,
Minia Campos-Domínguez
2   Department of Pediatric Dermatology, Hospital General Universitario Gregorio Marañón, Madrid, Spain
,
Javier Ordoñez 
1   Department of Pediatric Surgery, Hospital General Universitario Gregorio Marañón, Madrid, Spain
,
María Dolores Blanco Verdú
1   Department of Pediatric Surgery, Hospital General Universitario Gregorio Marañón, Madrid, Spain
,
María Fanjul
1   Department of Pediatric Surgery, Hospital General Universitario Gregorio Marañón, Madrid, Spain
,
Laura Pérez-Egido
1   Department of Pediatric Surgery, Hospital General Universitario Gregorio Marañón, Madrid, Spain
,
Juan Carlos de Agustín 
1   Department of Pediatric Surgery, Hospital General Universitario Gregorio Marañón, Madrid, Spain
› Institutsangaben Funding None.
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Abstract

Vulvar masses in children are an unusual finding but their differential diagnosis is extensive. In case of solid masses, rhabdomyosarcoma (RMS) must always be considered due to the fact that it is the most common tumor in external genitals during childhood. However, RMS has a radiological appearance very similar to juvenile xanthogranuloma (JXG). We present a 16-month-old girl with a 2 cm solid mass on her left labia majora, with four overlying cutaneous papules. After imaging tests, an excisional biopsy was programmed due to high malignancy suspicion. Histopathology of the mass and one of the papules was diagnostic for JXG. After a 12-month follow-up, the patient shows no signs of relapse or complication. Deep JXG is an uncommon entity in childhood and exceptional in the genital area. Therefore, it must be included in the differential diagnosis of a solid vulvar mass, especially if accompanying yellowish xanthomatous cutaneous lesions are present.

Keywords

vulvar mass - juvenile xanthogranuloma - rhabdomyosarcoma

Consent Statement

None of the photographs show recognizable persons.




Publikationsverlauf

Eingereicht: 04. Juli 2021

Angenommen: 23. November 2021

Artikel online veröffentlicht:
19. April 2022

© 2022. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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