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CC BY-NC-ND 4.0 · Arquivos Brasileiros de Neurocirurgia: Brazilian Neurosurgery 2023; 42(02): e181-e185
DOI: 10.1055/s-0041-1739271
Case Report | Relato de Caso

Ewing Sarcoma in the Sciatic Nerve: Case Report

Sarcoma de Ewing no Nervo Ciático: Relato de Caso
Robinson Antonio Menegotto Marques 
1   Department of Neurosurgery, Hospital Vita Curitiba, Curitiba, PR, Brazil
,
Adriana Hernandez Marques 
2   Medical School, Universidade Federal do Paraná (UFPR), Curitiba, Brazil
,
Amanda Hernandez Marques 
3   Medical School, Pontifícia Universidade Católica do Paraná (PUCPR), Curitiba, Brazil
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Abstract

Ewing sarcoma (ES) is a malignant neoplasm that affects bones and soft tissues, usually in young patients. Currently, ES is grouped with other tumors that share the same histological and genotypic characteristics, forming the Ewing Sarcoma Family of Tumors (ESFT), which includes ES of bone, extraosseous ES (peripheral neuroepithelioma), Askin tumor, and peripheral primitive neuroectodermal tumor (PNET). Its origin in peripheral nerves is extremely rare, making its diagnosis and treatment very challenging. We describe a case of a 27-year-old male with extraosseous ES originating in the sciatic nerve, which was surgically removed, and discuss the difficulties encountered in the management of this patient.

Resumo

O sarcoma de Ewing (SE) é uma neoplasia maligna que acomete ossos e partes moles, geralmente em pacientes jovens. Atualmente, o SE é agrupado com outros tumores que compartilham as mesmas características histológicas e genotípicas, formando os Tumores da Família do Sarcoma de Ewing (TFSE), que incluem o SE ósseo, o SE extraósseo (neuroepitelioma periférico), o tumor de Askin, e o tumor neuroectodérmico primitivo (TNEP) periférico. Sua origem em nervos periféricos é extremamente rara, o que torna o seu diagnóstico e tratamento um grande desafio. Descrevemos o caso de um homem de 27 anos com SE extraósseo originário no nervo ciático, que foi removido cirurgicamente, e discutimos as dificuldades encontradas no manejo desse paciente.

Keywords

Ewing sarcoma - peripheral nerves - primitive neuroectodermal tumor

Palavras-chave

sarcoma de Ewing - nervos periféricos - tumor neuroectodérmico primitivo


Publication History

Received: 15 April 2021

Accepted: 16 June 2021

Article published online:
02 February 2022

© 2022. Sociedade Brasileira de Neurocirurgia. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commecial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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