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CC BY 4.0 · European J Pediatr Surg Rep. 2021; 09(01): e68-e71
DOI: 10.1055/s-0041-1735595
Case Report

Clinical Quiz—A Rare Case of Anal Canal Duplication in the Context of Currarino Syndrome

Sean Jared Connor
1   Department of Paediatric Surgery, Chris Hani Baragwanath Hospital, Johannesburg, Gauteng, South Africa
2   University of the Witwatersrand School of Clinical Medicine, Johannesburg, Gauteng, South Africa
,
Giulia Brisighelli 
1   Department of Paediatric Surgery, Chris Hani Baragwanath Hospital, Johannesburg, Gauteng, South Africa
,
Nirav Patel
3   Department of Paediatric Surgery, University of the Witwatersrand, Johannesburg, Gauteng, South Africa
,
Marc A. Levitt
4   Department of Surgery, Colorectal and Pelvic Reconstructive Surgery, Children's National Hospital, Washington, District of Columbia, United States
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Abstract

Currarino syndrome (CS) is a rare condition that presents with any combination of a sacral defect, a presacral mass, and an anorectal malformation. This collection, referred to as Currarino's triad, may not necessarily present as all three abnormalities in the diagnosis of the syndrome. Anal canal duplication (ACD) is an even rarer occurrence. We present a case that lies on the CS spectrum with an associated ACD and discuss a complex surgical challenge that necessitated a customized management plan, devised through a multidisciplinary approach.

Keywords

currarino syndrome - anal canal - anorectal malformation - sacral defect - congenital abnormalities


Publication History

Received: 19 April 2021

Accepted: 05 July 2021

Article published online:
10 November 2021

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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