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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2021; 31(03): 707-709
DOI: 10.1055/s-0041-1735503
Case Report

A Triad of Unilateral Renal Dysgenesis with Ipsilateral Seminal Vesical and Ejaculatory Duct Obstruction: An Uncommon Urogenital Congenital Anomaly, Zinner Syndrome—A Case Report

Rajani Gorantla
1   Department of Radiodiagnosis, NRI Medical College and Hospital, Mangalagiri, Andhra Pradesh, India
,
Sameera Allu
1   Department of Radiodiagnosis, NRI Medical College and Hospital, Mangalagiri, Andhra Pradesh, India
,
Ankamma Rao
1   Department of Radiodiagnosis, NRI Medical College and Hospital, Mangalagiri, Andhra Pradesh, India
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Abstract

Zinner syndrome is a rare congenital anomaly of the urogenital system resulting from an in utero insult during the first trimester. This entity comprises a triad of unilateral renal agenesis/dysgenesis with ipsilateral seminal vesical and ejaculatory duct obstruction. This combination of urinary and genital abnormalities occurs because of the closely related embryological origin of these structures from the distal mesonephric (Wolffian) duct. Nearly 200 cases of seminal vesical cysts with ipsilateral renal agenesis have been reported in the literature. The affected person generally presents in early adulthood when the reproductive activity commences. In this report, we present a case of a 22-year-old male with complaints of painful ejaculation.

Keywords

Zinner syndrome - urogenital - mesonephric duct


Publication History

Article published online:
07 September 2021

© 2021. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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