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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2021; 31(02): 499-509
DOI: 10.1055/s-0041-1734335
Case Report

Preoperative Diagnosis of Suprasellar Hemangioblastoma with Four-Dimensional Computed Tomography Angiography: Case Report and Literature Review

Yi Tong
1   Department of Radiology, McGill University Health Center, Montreal, Quebec, Canada
,
Denis Sirhan
2   Department of Neurosurgery, Montreal Neurological Hospital and Institute, Montreal, Quebec, Canada
,
Maria Cortes
1   Department of Radiology, McGill University Health Center, Montreal, Quebec, Canada
3   Department of Radiology, Montreal Neurological Hospital and Institute, Montreal, Quebec, Canada
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Purpose Our case report presents the first case of suprasellar hemangioblastoma diagnosed preoperatively with dynamic computed tomography angiography (four-dimensional [4D] CTA) in a patient without Von Hippel-Lindau (VHL) disease. We illustrate the imaging characteristics of these exceedingly rare tumors and discuss the role of 4D CTA in confirming this diagnosis and guiding surgical management. Finally, we present a literature review of imaging findings, differential diagnosis, management, and prognosis.

Case A 39-year-old woman known for diabetes mellitus type II and dyslipidemia presented with headache, bitemporal hemianopsia, and mild hyperprolactinemia. Initial diagnosis of suprasellar meningioma separate from pituitary gland was revised to definitive diagnosis of suprasellar hemangioblastoma after 4D CTA.

Conclusion Suprasellar hemangioblastomas are extremely rare, often associated to VHL disease. They present as enhancing as suprasellar mass with prominent intra- and peritumoral vascular flow-voids on magnetic resonance imaging. 4D CTA confirms their vascular nature, demonstrates characteristic rapid shunting with feeding arteries, and enlarged draining veins, and is important in guiding surgical management.

4D CT angiography - dynamic CT angiography - hemangioblastoma - sella turcica


Publication History

Article published online:
03 September 2021

© 2021. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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