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CC BY 4.0 · European J Pediatr Surg Rep. 2021; 09(01): e65-e67
DOI: 10.1055/s-0041-1731274
Case Report

Severe Spontaneous Pneumomediastinum in a Girl with Cystic Fibrosis

Csaba Zsiborás
1   Department of Pediatrics, University of Pécs, Medical School, Pecs, Hungary
,
Mária Adonyi
1   Department of Pediatrics, University of Pécs, Medical School, Pecs, Hungary
,
József Stankovics
1   Department of Pediatrics, University of Pécs, Medical School, Pecs, Hungary
,
András Farkas
1   Department of Pediatrics, University of Pécs, Medical School, Pecs, Hungary
,
Peter Vajda
1   Department of Pediatrics, University of Pécs, Medical School, Pecs, Hungary
,
Barnabás Rózsai 
1   Department of Pediatrics, University of Pécs, Medical School, Pecs, Hungary
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Abstract

We report on an 11-year-old girl with cystic fibrosis who presented with thoracic pain and an extensive subcutaneous emphysema and subsequently developed progressive respiratory distress. The chest computed tomography revealed a huge pneumomediastinum. Due to the development of severe respiratory failure, urgent needle thoracocentesis was necessary that resulted in only temporary improvement. Therefore, under general anesthesia two mediastinal drains were introduced. Using active suction, the size of the pneumomediastinum decreased gradually and the drains were removed after 3 weeks. Here, we describe an extremely rare situation, when acute surgical intervention was necessary in a child with spontaneous pneumomediastinum.

Keywords

spontaneous pneumomediastinum - cystic fibrosis - mediastinal drainage


Publication History

Received: 24 January 2021

Accepted: 01 May 2021

Article published online:
01 October 2021

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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  • References

  • 1 Fitzwater JW, Silva NN, Knight CG, Malvezzi L, Ramos-Irizarry C, Burnweit CA. Management of spontaneous pneumomediastinum in children. J Pediatr Surg 2015; 50 (06) 983-986
    CrossrefPubMedGoogle Scholar
  • 2 Johnson JN, Jones R, Wills BK. Spontaneous pneumomediastinum. West J Emerg Med 2008; 9 (04) 217-218
    PubMedGoogle Scholar
  • 3 Chalumeau M, Le Clainche L, Sayeg N. et al. Spontaneous pneumomediastinum in children. Pediatr Pulmonol 2001; 31 (01) 67-75
    CrossrefPubMedGoogle Scholar
  • 4 Flume PA, Mogayzel Jr PJ, Robinson KA, Rosenblatt RL, Quittell L, Marshall BC. Clinical Practice Guidelines for Pulmonary Therapies Committee, Cystic Fibrosis Foundation Pulmonary Therapies Committee. Cystic fibrosis pulmonary guidelines: pulmonary complications: hemoptysis and pneumothorax. Am J Respir Crit Care Med 2010; 182 (03) 298-306
    CrossrefPubMedGoogle Scholar
  • 5 Benlamkaddem S, Berdai MA, Labib S, Harandou M. A case of spontaneous pneumomediastinum with subcutaneous emphysema in children. Children (Basel) 2018; 5 (02) 22
    PubMedGoogle Scholar
  • 6 Gerazounis M, Athanassiadi K, Kalantzi N, Moustardas M. Spontaneous pneumomediastinum: a rare benign entity. J Thorac Cardiovasc Surg 2003; 126 (03) 774-776
    CrossrefPubMedGoogle Scholar
  • 7 Bakhos CT, Pupovac SS, Ata A, Fantauzzi JP, Fabian T. Spontaneous pneumomediastinum: an extensive workup is not required. J Am Coll Surg 2014; 219 (04) 713-717
    CrossrefPubMedGoogle Scholar
  • 8 Tortajada-Girbés M, Moreno-Prat M, Ainsa-Laguna D, Mas S. Spontaneous pneumomediastinum and subcutaneous emphysema as a complication of asthma in children: case report and literature review. Ther Adv Respir Dis 2016; 10 (05) 402-409
    CrossrefPubMedGoogle Scholar
  • 9 Gasser CR, Pellaton R, Rochat CP. Pediatric spontaneous pneumomediastinum: narrative literature review. Pediatr Emerg Care 2017; 33 (05) 370-374
    CrossrefPubMedGoogle Scholar
  • 10 Gáti N, Kassai T, Prokopp T. et al. Pediatric tracheal injuries: report on 5 cases with special view on the role of bronchoscopy and management. Injury 2020
    PubMedGoogle Scholar