CC BY-NC-ND 4.0 · Journal of Clinical Interventional Radiology ISVIR
DOI: 10.1055/s-0041-1729465
Case Report

Atypical Moyamoya Disease Associated with Midaortic Syndrome

1  PDCC Neuroradiology, Department of Radiodiagnosis, SGPGI, Lucknow, UP, India
Vivek Singh
2  Department of Radiodiagnosis, SGPGI, Lucknow, UP, India
Chandradev Sahu
3  Department of Radiodiagnosis, Pt. JNMC, Raipur, Chhattisgarh, India
› Author Affiliations


We report a case of a 4-year-old boy who presented with moyamoya disease associated with midaortic syndrome. He had been treated for severe persistent hypertension until he suffered multiple episodes of seizure and cerebral ischemic attack. Cerebral angiography showed bilateral terminal internal carotid artery stenosis. Angiographic survey showed severe stenosis of abdominal aorta and bilateral proximal renal arteries. This is a very rare report of moyamoya disease with midaortic syndrome.

Publication History

Publication Date:
29 April 2021 (online)

© 2021. Indian Society of Vascular and Interventional Radiology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (

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