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CC BY-NC-ND 4.0 · Indian Journal of Neurotrauma 2022; 19(01): 044-046
DOI: 10.1055/s-0041-1729136
Case Report

Lhermitte–Duclos Disease: Incidental Finding in Traumatic Cerebral Hemorrhage

Hemant Kumar Beniwal
1   Department of Neurosurgery, Gandhi Medical College and Hospital, Secunderabad, Telangana, India
,
Thatikonda Satish
1   Department of Neurosurgery, Gandhi Medical College and Hospital, Secunderabad, Telangana, India
,
Gollapudi Prakash Rao
1   Department of Neurosurgery, Gandhi Medical College and Hospital, Secunderabad, Telangana, India
,
Musali Siddartha Reddy
1   Department of Neurosurgery, Gandhi Medical College and Hospital, Secunderabad, Telangana, India
,
Srikrishnaaditya Manne
1   Department of Neurosurgery, Gandhi Medical College and Hospital, Secunderabad, Telangana, India
› Author Affiliations Funding None.
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Abstract

Lhermitte–Duclos disease, also known as dysplastic cerebellar gangliocytoma, is a rare hamartomatous tumor localized in cerebellum. An association with Cowden syndrome is observed in 50% of cases who present with symptoms of increased intracranial pressure and cerebellar ataxia. These patients have specific magnetic resonance imaging and histopathological findings. Surgical resection is the treatment of choice. Here, we report a case of a young female with traumatic frontal hemorrhage associated with Lhermitte–Duclos disease.

Keywords

Lhermitte–Duclos disease - dysplastic cerebellar gangliocytoma - Cowden disease


Publication History

Article published online:
07 July 2021

© 2021. Neurotrauma Society of India. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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